뇌정맥혈전증으로 오인된 IgG4연관비후경수막염

IgG4-Related Hypertrophic Pachymeningitis Mimicking Cerebral Venous Thrombosis
  • 배정훈
  • 유준상
  • 이용경
  • 김예슬
  • 신수진
  • 외 1명

초록

Immunoglobulin G4-related hypertrophic pachymeningitis (IgG4-RHP) is an increasingly recognized manifestation of IgG4-related disease (IgG4-RD), which is a fibroinflammatory condition that can affect virtually any organ. The three hallmark histopathological features of IgG4-RD are lymphoplasmacytic infiltration of IgG4-positive plasma cells, storiform fibrosis, and obliterative phlebitis. We report a case of biopsy-confirmed IgG4-RHP that was initially misdiagnosed as cerebral venous thrombosis.

키워드

IgG4-related hypertrophic pachymeningitisIntracranial thrombosisHistopathology
제목
뇌정맥혈전증으로 오인된 IgG4연관비후경수막염
제목 (타언어)
IgG4-Related Hypertrophic Pachymeningitis Mimicking Cerebral Venous Thrombosis
저자
배정훈유준상이용경김예슬신수진김현영
DOI
10.17340/jkna.2018.3.14
발행일
2018-08
저널명
대한신경과학회지
36
3
페이지
207 ~ 209