Extensive and aggressive growth of adenoid cystic carcinoma in the lacrimal gland

초록

Adenoid cystic carcinoma (ACC) in the lacrimal gland is a very rare disease with poor overall prog-nosis. Its primary treatment is surgical excision, including orbital exenteration and radical orbitec-tomy, which is combined with radiotherapy and chemotherapy. Age, histopathologic type, bone invasion, and tumor extent are known factors that affect the prognosis of ACC. Furthermore, peri-neural invasion is highly associated with local tumor recurrence and tumor base invasion. Here, we report a rare case of ACC in the lacrimal gland with superior sagittal sinus invasion that re-peatedly recurred after the surgical excision. © 2020 Korean Cleft Palate-Craniofacial Association.

키워드