좌측 중지의 상피 양혈관내피증

초록

Epithelioid hemangioendothelioma is a recently described vascular neoplasm characterized by epithelioid endothelial linings and its borderline biologic behavior. We report a case of epithelioid hemangioendothelioma in a 6-year-old male. The tumor was presented as a non-tender dermal nodule on the left middle finger. The microscopic sections revealed irregular proliferation of vas- cular channels lined by epithelioid cells with histiocytoid features and frequent intracytoplasmic vacuoles, mimicking so called signet ring cells. Immunohistochemical stainings for factor VIII and vimentin were positive both in epithelioid and vacuolated endothelial cell. Electron micro- scopic finding reveals abundant intermediate filaments.

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