Pediatric split liver transplantation after Fontan procedure in left isomerism combined with biliary atresia: A case report

  • Youn, Joong Kee
  • Lee, Jeong-Moo
  • Yi, Nam-Joon
  • Choi, Young Rok
  • Suh, Suk-Won
  • 외 9명
Citations

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6
Citations

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7

초록

LI is a subset of the heterotaxy syndrome and a rare birth defect that involves the heart and other organs. It can be combined with extracardiac abnormalities, especially BA. CHD can be associated with LI in up to 15% of cases, although it is rare in BA. Pediatric LT for a child with ESLD due to BA combined with LI and CHD is a challenging issue for a transplant surgeon. Herein, we report a successful split LT on a three-yr-old boy with LI who survived after a Fontan procedure due to single ventricle, but who suffered from HPS associated with BA.

키워드

biliary atresialeft isomerismFontan operationhepatopulmonary syndromeliver transplantationSITUS-INVERSUSHEPATOPULMONARY SYNDROMEOPERATIONMORTALITYSURGERYCOMPLICATIONSCIRCULATIONPREDICTORSOUTCOMESCHILDREN
제목
Pediatric split liver transplantation after Fontan procedure in left isomerism combined with biliary atresia: A case report
저자
Youn, Joong KeeLee, Jeong-MooYi, Nam-JoonChoi, Young RokSuh, Suk-WonYou, TaeLee, Kwang-WoongJung, Chul-WooLee, Ji-wonBae, Eun-JungKo, Jae SungKim, Woong-HanPark, Kwi-WonSuh, Kyung-Suk
DOI
10.1111/petr.12364
발행일
2014-12
유형
Article
저널명
Pediatric Transplantation
18
8
페이지
E274 ~ E279