Pediatric split liver transplantation after Fontan procedure in left isomerism combined with biliary atresia: A case report

  • Youn, Joong Kee; 
  • Lee, Jeong-Moo; 
  • Yi, Nam-Joon; 
  • Choi, Young Rok; 
  • Suh, Suk-Won; 
  • 외 9명
Citations

WEB OF SCIENCE

6
Citations

SCOPUS

7

초록

LI is a subset of the heterotaxy syndrome and a rare birth defect that involves the heart and other organs. It can be combined with extracardiac abnormalities, especially BA. CHD can be associated with LI in up to 15% of cases, although it is rare in BA. Pediatric LT for a child with ESLD due to BA combined with LI and CHD is a challenging issue for a transplant surgeon. Herein, we report a successful split LT on a three-yr-old boy with LI who survived after a Fontan procedure due to single ventricle, but who suffered from HPS associated with BA.

키워드

biliary atresia; left isomerism; Fontan operation; hepatopulmonary syndrome; liver transplantation; SITUS-INVERSUS; HEPATOPULMONARY SYNDROME; OPERATION; MORTALITY; SURGERY; COMPLICATIONS; CIRCULATION; PREDICTORS; OUTCOMES; CHILDREN
제목
Pediatric split liver transplantation after Fontan procedure in left isomerism combined with biliary atresia: A case report
저자
Youn, Joong Kee; Lee, Jeong-Moo; Yi, Nam-Joon; Choi, Young Rok; Suh, Suk-Won; You, Tae; Lee, Kwang-Woong; Jung, Chul-Woo; Lee, Ji-won; Bae, Eun-Jung; Ko, Jae Sung; Kim, Woong-Han; Park, Kwi-Won; Suh, Kyung-Suk
DOI
10.1111/petr.12364
발행일
2014-12
유형
Article
저널명
Pediatric Transplantation
권
18
호
8
페이지
E274 ~ E279